
Paroxysmal Nocturnal Hemoglobinuria - StatPearls - NCBI Bookshelf
2023年7月31日 · Paroxysmal nocturnal hemoglobinuria (PNH) is a rare disease that presents clinically with a variety of nonspecific symptoms. It causes complications mainly through …
Paroxysmal nocturnal hemoglobinuria - Wikipedia
Paroxysmal nocturnal hemoglobinuria (PNH) is a rare, acquired, [1] life-threatening disease of the blood characterized by destruction of red blood cells by the complement system, a part of the …
Paroxysmal nocturnal hemoglobinuria: pathophysiology, natural history ...
Paroxysmal nocturnal hemoglobinuria (PNH), first described in the 18th century, is characterized by the typical clinical triad of hemolytic anemia, bone marrow failure, and propensity to …
Paroxysmal Nocturnal Hemoglobinuria: Practice Essentials ...
2024年6月25日 · Paroxysmal nocturnal hemoglobinuria (PNH) is a clonal hematopoietic stem cell (HSC) disease. It is a rare, chronic, debilitating disorder that most frequently presents in early...
Control of hemolysis in patients with PNH | Blood | American …
2021年11月18日 · Paroxysmal nocturnal hemoglobinuria (PNH) is characterized by the triad of intravascular hemolysis (IVH), a tendency to thrombosis, and an element of bone marrow failure.
Paroxysmal Nocturnal Hemoglobinuria: Causes, Symptoms
When discussing Paroxysmal Nocturnal Hemoglobinuria (PNH), the “classic triad” refers to a set of three key clinical manifestations that have historically been associated with the disease. It’s …
The Management of Paroxysmal Nocturnal Hemoglobinuria: …
PNH is characterized by the triad of acquired corpuscular hemolysis, thrombophilia, and bone marrow failure. The intravascular destruction of PNH red blood cells causes chronic, often …
British Journal of Haematology | Wiley Online Library
2021年8月5日 · Paroxysmal nocturnal haemoglobinuria (PNH) is a rare haematological disease characterized by the clinical triad: complement-mediated intravascular haemolysis, severe …
The management of paroxysmal nocturnal hemoglobinuria: recent ... - PubMed
PNH is a rare clonal hematopoietic stem disorder clinically characterized by the triad of chronic complement-mediated hemolysis, thrombosis, and bone marrow failure. While median survival …
Paroxysmal Nocturnal Hemoglobinuria in the Differential …
2017年2月2日 · Paroxysmal nocturnal hemoglobinuria is a rare, life-threatening, genetic hematological disorder characterized by hemolysis of the red blood cells. The classic …