Budd-Chiari Syndrome - StatPearls - NCBI Bookshelf
2020年8月8日 · Budd-Chiari syndrome (BCS) is an uncommon disorder defined as hepatic venous outflow tract obstruction, which is independent of the level or mechanism of obstruction, given the obstruction is not due to pericardial disease, cardiac disease, or sinusoidal obstruction syndrome (veno-occlusive disease).[1]
Budd–Chiari syndrome - Wikipedia
Budd–Chiari syndrome is a very rare condition, affecting one in a million adults. [1][2] The condition is caused by occlusion of the hepatic veins (usually due to a blood clot) that drain the liver. The symptoms are non-specific and vary widely, but it may present with the classical triad of: liver enlargement.
Budd-Chiari syndrome: Etiology, pathogenesis and diagnosis
Budd-Chiari syndrome is a congestive hepatopathy caused by blockage of hepatic veins. This syndrome occurs in 1/100 000 in the general population. Hypercoagulable state could be identified in 75% of the patients; more than one etiologic factor …
Diagnosis and therapy of Budd Chiari syndrome - PMC
Budd-Chiari syndrome is described as a disorder characterized by the obstruction of hepatic venous outflow. The first description of the syndrome was done by George Budd in 1846. The etiology of the disease is multifactorial and requires differential diagnosing.
Budd-Chiari Syndrome - PubMed
2023年1月30日 · Budd-Chiari syndrome (BCS) is an uncommon disorder defined as hepatic venous outflow tract obstruction, which is independent of the level or mechanism of obstruction, given the obstruction is not due to pericardial disease, cardiac disease, or sinusoidal obstruction syndrome (veno-occlusive disease) …
Hepatic Venous Outflow Obstruction (Budd-Chiari Syndrome)
The prevalence of primary hepatic venous outflow obstruction, or Budd-Chiari syndrome, is 1 case per million persons per year. Predisposing factors, including hereditary and acquired hypercoagulable states, can be identified in up to 75% of affected patients; multiple disorders are found in up to 35%.Up to 50% of cases are associated with polycythemia vera or other myeloproliferative neoplasms ...
Current knowledge in pathophysiology and management of Budd-Chiari …
Budd-Chiari syndrome and non-cirrhotic non-tumoral portal vein thrombosis are 2 rare disorders, with several similarities that are categorized under the term splanchnic vein thrombosis. Both disorders are frequently associated with an underlying prothrombotic disorder. They can cause severe portal h …
Hepatic Venous Outflow Obstruction (Budd-Chiari Syndrome)
Predisposing factors for Budd-Chiari, including hereditary and acquired hypercoagulable states, can be identified in up to 75% of affected patients; multiple disorders are found in up to 35%. Up to 50% of cases of Budd-Chiari are associated with polycythemia vera or other myeloproliferative neoplasms (which entail a 1% risk of Budd-Chiari syndrome)
Budd-Chiari Syndrome - Budd-Chiari Syndrome - MSD Manuals
Budd-Chiari syndrome is obstruction of hepatic venous outflow that originates anywhere from the small hepatic veins inside the liver to the inferior vena cava and right atrium. Manifestations range from no symptoms to fulminant liver failure. If suspected, initial testing is Doppler ultrasonography.
Budd–Chiari syndrome: a review by an expert panel
Budd–Chiari syndrome is defined as hepatic venous outflow obstruction at any level from the small hepatic veins to the junction of the inferior vena cava and the right atrium, regardless of the cause of obstruction. Outflow obstruction caused by hepatic veno-occlusive disease and cardiac disorders is excluded from this definition.